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1Department of Paediatrics, Kalinga Institute of Medical Sciences (KIMS), KIIT Deemed University, Patia, Bhubaneswar, Odisha, India
2Department of Radiodiagnosis, Kalinga Institute of Medical Sciences (KIMS), KIIT Deemed University, Patia, Bhubaneswar, Odisha, India
MR Behera
, M Mohapatra
Takayasu arteritis (TA) is a chronic, idiopathic large vessel vasculitis mainly affecting the aorta and its major branches. It is one of the common causes of reno-vascular hypertension in Indian children. We report a ten-year-old boy who presented with hypertensive encephalopathy, proteinuria, and haematuria without any renal dysfunction. He was initially diagnosed to be a case of acute post streptococcal glomerulonephritis, but detailed clinical examination and haemato-radiological investigations revealed Takayasu arteritis, type V (P+). He had unilateral severe renal artery stenosis along with a small kidney and an aberrant renal artery on left side. He is found to have resistant hypertension, unresponsive to multiple anti-hypertensive drugs, and had a fatal outcome. This case illustrates renal involvement in TA and the significance of four-limb blood pressure measurement in any non-obese child with hypertension. Furthermore, the possible role of aberrant renal artery in the pathogenesis of resistant hypertension is discussed.
Cite this article as: Behera MR, Mohapatra M, Yadav SK. Takayasu Arteritis with Severe Renal Artery Stenosis and an Aberrant Renal Artery in a Child: A Case Report and Discussion. Mediterr J Rheumatol 2023;34(3):381-5.
Article Submitted: 19 Jul 2021; Revised Form: 1 Jun 2022; Article Accepted: 15 Jun 2022; Available Online: 27 Jul 2023
https://doi.org/10.31138/mjr.230727.bt
This work is licensed under a Creative Commons Attribution 4.0 International License.
©2023 The Author(s).
